The horseshoe kidney is a common anatomical variation of de renal system that is often asymptomatic, however the concomitance with congenital abnormalities in these patients could result in the development of symptoms because of the renal or cardiovascular complications and renal tumors that arise predominantly as malignancies. This job describes the anatomic variations of a horseshoe kidney associated to three independent ureters and a hilium arteriovenous variant consistent in four renal arteries and three renal veins, an incidental dissection case found in the laboratory of Costa Rica’s University Medicine School. Moreover, an actualized literature review of the horseshoe kidney is presented so that health professionals could be able to detect it and diagnose it, and associate it with the congenital abnormalities described above to prevent its complications.

Horseshoe kidneys; metanephros; Wilms tumor